Follow
Helen Cooper
Helen Cooper
Research specialist, Åbo Akademi University
Verified email at abo.fi
Title
Cited by
Cited by
Year
Mitochondrial ROS produced via reverse electron transport extend animal lifespan
F Scialo, A Sriram, D Fernandez-Ayala, N Gubina, M Lohmus, G Nelson, ...
Cell metabolism 23 (4), 725-734, 2016
3472016
In vivo functional analysis of the human mitochondrial DNA polymerase POLG expressed in cultured human cells
JN Spelbrink, JM Toivonen, GAJ Hakkaart, JM Kurkela, HM Cooper, ...
Journal of Biological Chemistry 275 (32), 24818-24828, 2000
2302000
Mitochondrial nucleoid interacting proteins support mitochondrial protein synthesis
J He, HM Cooper, A Reyes, M Di Re, H Sembongi, TR Litwin, J Gao, ...
Nucleic acids research 40 (13), 6109-6121, 2012
2192012
The human SIRT3 protein deacetylase is exclusively mitochondrial
HM Cooper, JN Spelbrink
Biochemical Journal 411 (2), 279-285, 2008
1552008
Infantile-onset spinocerebellar ataxia and mitochondrial recessive ataxia syndrome are associated with neuronal complex I defect and mtDNA depletion
AH Hakonen, S Goffart, S Marjavaara, A Paetau, H Cooper, K Mattila, ...
Human molecular genetics 17 (23), 3822-3835, 2008
1512008
Twinkle mutations associated with autosomal dominant progressive external ophthalmoplegia lead to impaired helicase function and in vivo mtDNA …
S Goffart, HM Cooper, H Tyynismaa, S Wanrooij, A Suomalainen, ...
Human molecular genetics 18 (2), 328-340, 2009
1502009
Human mitochondrial DNA-protein complexes attach to a cholesterol-rich membrane structure
JM Gerhold, Ş Cansiz-Arda, M Lõhmus, O Engberg, A Reyes, ...
Scientific reports 5 (1), 15292, 2015
1072015
Human C4orf14 interacts with the mitochondrial nucleoid and is involved in the biogenesis of the small mitochondrial ribosomal subunit
J He, HM Cooper, A Reyes, M Di Re, L Kazak, SR Wood, CC Mao, ...
Nucleic acids research 40 (13), 6097-6108, 2012
972012
ATPase-deficient mitochondrial inner membrane protein ATAD3A disturbs mitochondrial dynamics in dominant hereditary spastic paraplegia
HM Cooper, Y Yang, E Ylikallio, R Khairullin, R Woldegebriel, KL Lin, ...
Human molecular genetics 26 (8), 1432-1443, 2017
842017
A new splice variant of the mouse SIRT3 gene encodes the mitochondrial precursor protein
HM Cooper, JY Huang, E Verdin, JN Spelbrink
PloS one 4 (3), e4986, 2009
622009
Mitochondrial antibodies in primary biliary cirrhosis: IV. Significance of membrane structure for the complement-fixing antigen
PA Berg, IM Roitt, D Doniach, HM Cooper
Immunology 17 (2), 281, 1969
481969
Sphingosine kinase 1 overexpression induces MFN2 fragmentation and alters mitochondrial matrix Ca2+ handling in HeLa cells
I Pulli, C Löf, T Blom, MY Asghar, T Lassila, N Bäck, KL Lin, JH Nyström, ...
Biochimica et Biophysica Acta (BBA)-Molecular Cell Research 1866 (9), 1475-1486, 2019
142019
Severe neonatal MEGDHEL syndrome with a homozygous truncating mutation in SERAC1
V Fellman, R Banerjee, KL Lin, I Pulli, H Cooper, H Tyynismaa, J Kallijärvi
Biochimica et Biophysica Acta (BBA)-Molecular Basis of Disease 1868 (1), 166298, 2022
52022
ATPase-deficient ATAD3A alters mitochondrial dynamics in hereditary spastic paraplegia
RA Woldegebriel, HM Cooper, EA Ylikallio, R Khairullin, K Lin, L Euro, ...
European Journal of Human Genetics 26, 111-112, 2018
2018
Regulating mitochondrial function: The roles of SIRT3 as a mitochondrial protein deacetylase and the functions of the Twinkle helicase in mitochondrial DNA maintenance
H Cooper
Tampere University Press, 2009
2009
Twinkle mutations associated with autosomal dominant progressive external ophthalmoplegia lead to impaired helicase function and in vivo mtDNA replication stalling.
S Goffart, HM Cooper, H Tyynismaa, S Wanrooij, A Suomalainen, ...
2008
BBA-Molecular Basis of Disease
V Fellman, R Banerjee, KL Lin, I Pulli, H Cooper, H Tyynismaa, J Kallijärvi
ATpase-deficient mitochondrial inner membrane protein ATAD3a disturbs mitochondrial dynamics in dominant hereditary spastic paraplegia
R Khairullin, L Euro, R Woldegebriel, S Kaakkola, K Lin, E Ylikallio, ...
The system can't perform the operation now. Try again later.
Articles 1–18