This document is the result of an European Consensus conference which took place in
Artimino, Tuscany, Italy, in March 2001 involving 33 experts on nutrition in patients with cystic …

Developments in managing CF continue to drive dramatic improvements in survival. As
newborn screening rolls-out across Europe, CF centres are increasingly caring for cohorts of …

… 44 Le Brun PPH, Brimicombe RW, van Doorne H, Heijerman HGM. The cleaning and
disinfection of nebulizers used at home and in a cystic fibrosis center. Eur Hosp Pharm 2000; …

Background Cystic fibrosis transmembrane conductance regulator (CFTR) modulators correct
the basic defect caused by CFTR mutations. Improvements in health outcomes have been …

Identifying subjects with cystic fibrosis (CF) who may benefit from cystic fibrosis transmembrane
conductance regulator (CFTR)–modulating drugs is time-consuming, costly, and …

In vitro drug tests using patient-derived stem cell cultures offer opportunities to individually
select efficacious treatments. Here, we provide a study that demonstrates that in vitro drug …

The improved survival in people with cystic fibrosis has led to an increasing number of
patients reaching adulthood. This trend is likely to be maintained over the next decades, …

Background: Pulmonary administration of colistin is one of the antimicrobial treatments used
in Cystic Fibrosis (CF) patients chronically infected with Pseudomonas aeruginosa. Dry …

The aim of the present study was to perform a proof of principle study with a new colistin dry
powder inhalation system in six healthy volunteers and five patients with cystic fibrosis. All …

Bronchial hyperresponsiveness is present in 40–60% of adult patients with cystic fibrosis (CF).
Drugs which alter airway hyperresponsiveness have not yet been studied in CF. In this …